肝臓の粘液性嚢胞性新生物（MCN-L）：文献のまれなプレゼンテーションとレビュー

肝臓の粘液性嚢胞性新生物（MCN-L（以前は膀胱腫瘍または膀胱癌と呼ばれていた）は、肝臓の実質内で発生する、またはそれほど頻繁ではない肝臓胆管で発生するまれな嚢胞性腫瘍です。すべての肝嚢胞のうち。MCN-Lの鑑別診断には、胆管乳頭腫瘍（IPNB）、嚢胞性変化を伴う肝内胆管癌、エキノカッカル嚢胞、エキノカッカル嚢胞、および単純な嚢胞浸潤MCNは、非侵襲的MCNSとのみ差別化できます。卵巣型間質の存在のための顕微鏡評価。術中生検および凍結切片は、MCNを他の嚢胞性肝臓病変と区別するために不可欠です。まれなプレゼンテーションと不十分な認識は、しばしば誤った初期または遅延診断または誤診につながります。

Mucinous cystic neoplasms of the liver (MCN-L, (previously referred to as cystadenomas or cystadenocarcinoma) are rare cystic tumors that occur within the liver parenchyma, or less frequently, in the extrahepatic bile ducts. They are reported to account for <5% of all liver cysts. The differential diagnosis of MCN-L includes intraductal papillary neoplasm of the bile duct (IPNB), intrahepatic cholangiocarcinoma with cystic change, echinococcal cyst, and a simple cyst. Invasive MCNs can only be differentiated from non-invasive MCNs by microscopic evaluation for the presence of ovarian-type stroma. Intraoperative biopsy and frozen section(s) are essential to differentiate MCNs from other cystic liver lesions. The treatment of choice is complete excision and can result in excellent survival with initial correct diagnosis. But its rare presentation and insufficient recognition frequently lead to an incorrect initial or delayed diagnosis or misdiagnosis.